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Title
Synaptic dysfunction in human neurons with autism-associated deletions in PTCHD1-AS
Source
Biological Psychiatry
Date
2020
Author
Ross, P. Joel
;
Zhang, Wen-Bo
;
Mok, Rebecca S.F.
;
Zaslavsky, Kirill
;
Deneault, Eric
;
D’Abate, Lia
;
Rodrigues, Deivid C.
;
Yuen, Ryan K.C.
;
Faheem, Muhammad
;
Mufteev, Marat
;
Piekna, Alina
;
Wei, Wei
;
Pasceri, Peter
;
Landa, Rebecca J.
;
Nagy, Andras
;
Varga, Balazs
;
Salter, Michael W.
;
Scherer, Stephen W.
;
Ellis, James
Genre
Journal Article
Abstract
Background The Xp22.11 locus that encompasses PTCHD1, DDX53, and the long noncoding RNA PTCHD1-AS is frequently disrupted in male subjects with...
Volume
87
Issue
2
Start Page
139
DOI
10.1016/j.biopsych.2019.07.014
Publication Status
PUBLISHED
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Title
Shifts in ribosome engagement impact key gene sets in neurodevelopment and ubiquitination in Rett Syndrome
Source
Cell Reports
Date
2020
Author
Rodrigues, Deivid C.
;
Mufteev, Marat
;
Weatheritt, Robert J.
;
Djuric, Ugljesa
;
Ha, Kevin C.H.
;
Ross, P. Joel
;
Wei, Wei
;
Piekna, Alina
;
Sartori, Maria A.
;
Byres, Loryn
;
Mok, Rebecca S.F.
;
Zaslavsky, Kirill
;
Pasceri, Peter
;
Diamandis, Phedias
;
Morris, Quaid
;
Blencowe, Benjamin J.
;
Ellis, James
Genre
Journal Article
Abstract
Regulation of translation during human development is poorly understood, and its dysregulation is associated with Rett syndrome (RTT). To discover...
Volume
30
Issue
12
Start Page
4179
DOI
10.1016/j.celrep.2020.02.107
Publication Status
PUBLISHED
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Title
Modeling neuronal consequences of autism-associated gene regulatory variants with human induced pluripotent stem cells
Source
Molecular Autism
Date
2020
Author
Ross, P. Joel
;
Mok, Rebecca S. F.
;
Smith, Brandon S.
;
Rodrigues, Deivid C.
;
Mufteev, Marat
;
Scherer, Stephen W.
;
Ellis, James
Genre
Journal Article
Abstract
Genetic factors contribute to the development of autism spectrum disorder (ASD), and although non-protein-coding regions of the genome are being...
Volume
11
Issue
1
DOI
10.1186/s13229-020-00333-6
Publication Status
PUBLISHED
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Title
Control of tong-term synaptic potentiation and learning by alternative splicing of the NMDA receptor subunit GluN1
Source
Cell Reports
Date
2019
Author
Sengar, Ameet S.
;
Li, Hongbin
;
Zhang, Wenbo
;
Leung, Celeste
;
Ramani, Arun K.
;
Saw, Ner Mu
;
Wang, Yongqian
;
Tu, YuShan
;
Ross, P. Joel
;
Scherer, Stephen W.
;
Ellis, James
;
Brudno, Michael
;
Jia, Zhengping
;
Salter, Michael W.
Genre
Journal Article
Abstract
NMDA receptors (NMDARs) are critical for physiological synaptic plasticity, learning, and memory and for pathological plasticity and neuronal death...
Volume
29
Issue
13
Start Page
4285
DOI
10.1016/j.celrep.2019.11.087
Publication Status
PUBLISHED
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Title
SHANK2 mutations associated with autism spectrum disorder cause hyperconnectivity of human neurons
Source
Nature Neuroscience
Date
2019
Author
Zaslavsky, Kirill
;
Zhang, Wen-Bo
;
McCready, Fraser P.
;
Rodrigues, Deivid C.
;
Deneault, Eric
;
Loo, Caitlin
;
Zhao, Melody
;
Ross, P. Joel
;
El Hajjar, Joelle
;
Romm, Asli
;
Thompson, Tadeo
;
Piekna, Alina
;
Wei, Wei
;
Wang, Zhuozhi
;
Khattak, Shahryar
;
Mufteev, Marat
;
Pasceri, Peter
;
Scherer, Stephen W.
;
Salter, Michael W.
;
Ellis, James
Genre
Journal Article
Abstract
Heterozygous loss-of-function mutations in SHANK2 are associated with autism spectrum disorder (ASD). We generated cortical neurons from induced...
Volume
22
Issue
4
Start Page
556
DOI
10.1038/s41593-019-0365-8
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Title
Complete disruption of autism-susceptibility genes by gene editing predominantly reduces functional connectivity of isogenic human neurons
Source
Stem Cell Reports
Date
2018
Author
Deneault, Eric
;
White, Sean H.
;
Rodrigues, Deivid C.
;
Ross, P. Joel
;
Faheem, Muhammad
;
Zaslavsky, Kirill
;
Wang, Zhuozhi
;
Alexandrova, Roumiana
;
Pellecchia, Giovanna
;
Wei, Wei
;
Piekna, Alina
;
Kaur, Gaganjot
;
Howe, Jennifer L.
;
Kwan, Vickie
;
Thiruvahindrapuram, Bhooma
;
Walker, Susan
;
Lionel, Anath C.
;
Pasceri, Peter
;
Merico, Daniele
;
Yuen, Ryan K.C.
;
Singh, Karun K.
;
Ellis, James
;
Scherer, Stephen W.
Genre
Journal Article
Abstract
Autism spectrum disorder (ASD) is phenotypically and genetically heterogeneous. We present a CRISPR gene editing strategy to insert a protein tag...
Volume
11
Issue
5
Start Page
1211
DOI
10.1016/j.stemcr.2018.10.003
Publication Status
PUBLISHED
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Title
MECP2 Is post-transcriptionally regulated during human neurodevelopment by combinatorial action of RNA-binding proteins and miRNAs
Source
Cell Reports
Date
2016
Author
Rodrigues, Deivid C.
;
Kim, Dae-Sung
;
Yang, Guang
;
Zaslavsky, Kirill
;
Ha, Kevin C.H.
;
Mok, Rebecca S.F.
;
Ross, P. Joel
;
Zhao, Melody
;
Piekna, Alina
;
Wei, Wei
;
Blencowe, Benjamin J.
;
Morris, Quaid
;
Ellis, James
Genre
Journal Article
Volume
17
Issue
3
Start Page
720
DOI
10.1016/j.celrep.2016.09.049
Publication Status
PUBLISHED
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Title
Fyn Kinase regulates GluN2B subunit-dominant NMDA receptors in human induced pluripotent stem cell-derived neurons
Source
Scientific Reports
Date
2016
Author
Zhang, Wen-Bo
;
Ross, P. Joel
;
Tu, YuShan
;
Wang, Yongqian
;
Beggs, Simon
;
Sengar, Ameet S.
;
Ellis, James
;
Salter, Michael W.
Genre
Journal Article
Volume
6
Issue
1
Start Page
23837
DOI
10.1038/srep23837
Publication Status
PUBLISHED
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Title
Human induced pluripotent stem cell derived neurons as a model for Williams-Beuren syndrome
Source
Molecular Brain
Date
2015
Author
Khattak, Shahryar
;
Brimble, Elise
;
Zhang, Wenbo
;
Zaslavsky, Kirill
;
Strong, Emma
;
Ross, P. Joel
;
Hendry, Jason
;
Mital, Seema
;
Salter, Michael W.
;
Osborne, Lucy R.
;
Ellis, James
Genre
Journal Article
Volume
8
Issue
1
Start Page
77
DOI
10.1186/s13041-015-0168-0
Publication Status
PUBLISHED
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Title
MECP2e1 isoform mutation affects the form and function of neurons derived from Rett syndrome patient iPS cells
Source
Neurobiology of Disease
Date
2015
Author
Djuric, Ugljesa
;
Cheung, Aaron Y.L.
;
Zhang, Wenbo
;
Mok, Rebecca S.
;
Lai, Wesley
;
Piekna, Alina
;
Hendry, Jason A.
;
Ross, P. Joel
;
Pasceri, Peter
;
Kim, Dae-Sung
;
Salter, Michael W.
;
Ellis, James
Genre
Journal Article
Volume
76
Start Page
37
DOI
10.1016/j.nbd.2015.01.001
Publication Status
PUBLISHED
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Title
Optimizing neuronal differentiation from induced pluripotent stem cells to model ASD
Source
Frontiers in Cellular Neuroscience
Date
2014
Author
Kim, Dae-Sung
;
Ross, P. Joel
;
Zaslavsky, Kirill
;
Ellis, James
Genre
Journal Article
Volume
8
DOI
10.3389/fncel.2014.00109
Publication Status
PUBLISHED
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Title
MBNL proteins repress ES-cell-specific alternative splicing and reprogramming
Source
Nature
Date
2013
Author
Han, Hong
;
Irimia, Manuel
;
Ross, P. Joel
;
Sung, Hoon-Ki
;
Alipanahi, Babak
;
David, Laurent
;
Golipour, Azadeh
;
Gabut, Mathieu
;
Michael, Iacovos P.
;
Nachman, Emil N.
;
Wang, Eric
;
Trcka, Dan
;
Thompson, Tadeo
;
O’Hanlon, Dave
;
Slobodeniuc, Valentina
;
Barbosa-Morais, Nuno L.
;
Burge, Christopher B.
;
Moffat, Jason
;
Frey, Brendan J.
;
Nagy, Andras
;
Ellis, James
;
Wrana, Jeffrey L.
;
Blencowe, Benjamin J.
Genre
Journal Article
Volume
498
Issue
7453
Start Page
241
DOI
10.1038/nature12270
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Title
MEF2 negatively regulates learning-induced structural plasticity and memory formation
Source
Nature Neuroscience
Date
2012
Author
Cole, Christina J
;
Mercaldo, Valentina
;
Restivo, Leonardo
;
Yiu, Adelaide P
;
Sekeres, Melanie J
;
Han, Jin-Hee
;
Vetere, Gisella
;
Pekar, Tetyana
;
Ross, P Joel
;
Neve, Rachael L
;
Frankland, Paul W
;
Josselyn, Sheena A
Genre
Journal Article
Volume
15
Issue
9
Start Page
1255
DOI
10.1038/nn.3189
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Title
Assembly of helper-dependent adenovirus DNA into chromatin promotes efficient gene expression
Source
Journal of Virology
Date
2011
Author
Ross, P. J.
;
Kennedy, M. A.
;
Christou, C.
;
Risco Quiroz, M.
;
Poulin, K. L.
;
Parks, R. J.
Genre
Journal Article
Volume
85
Issue
8
Start Page
3950
DOI
10.1128/JVI.01787-10
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Title
Spine growth in the anterior cingulate cortex is necessary for the consolidation of contextual fear memory
Source
Proceedings of the National Academy of Sciences
Date
2011
Author
Vetere, G.
;
Restivo, L.
;
Cole, C. J.
;
Ross, P. J.
;
Ammassari-Teule, M.
;
Josselyn, S. A.
;
Frankland, P. W.
Genre
Journal Article
Volume
108
Issue
20
Start Page
8456
DOI
10.1073/pnas.1016275108
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Title
Modeling complex neuropsychiatric disease with induced pluripotent stem cells
Source
F1000 Biology Reports
Date
2010
Author
Ellis, James P.
;
Ross, P. Joel
Genre
Journal Article
Volume
2
DOI
10.3410/B2-84
Publication Status
PUBLISHED
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Title
Host cell detection of noncoding stuffer DNA contained in helper-dependent adenovirus vectors leads to epigenetic repression of transgene expression
Source
Journal of Virology
Date
2009
Author
Ross, P. J.
;
Kennedy, M. A.
;
Parks, R. J.
Genre
Journal Article
Volume
83
Issue
17
Start Page
8409
DOI
10.1128/JVI.00796-09
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Title
Construction and characterization of adenovirus vectors
Source
Cold Spring Harbor Protocols
Date
2009
Author
Ross, P. J.
;
Parks, R. J.
Genre
Journal Article
Abstract
Genetically modified adenoviruses (Ads) make attractive vectors for the delivery of exogenous DNA to mammalian cells for basic science and gene...
Volume
2009
Issue
5
DOI
10.1101/pdb.prot5011
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Title
The inflammasome recognizes cytosolic microbial and host DNA and triggers an innate immune response
Source
Nature
Date
2008
Author
Muruve, Daniel A.
;
Pétrilli, Virginie
;
Zaiss, Anne K.
;
White, Lindsay R.
;
Clark, Sharon A.
;
Ross, P. Joel
;
Parks, Robin J.
;
Tschopp, Jurg
Genre
Journal Article
Volume
452
Issue
7183
Start Page
103
DOI
10.1038/nature06664
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Title
Helper-dependent adenovirus vectors elicit intact innate but attenuated adaptive host immune responses in vivo
Source
Journal of Virology
Date
2004
Author
Muruve, Daniel A.
;
Cotter, Matthew J.
;
Zaiss, Anne K.
;
White, Lindsay R.
;
Liu, Qiang
;
Chan, Trevor
;
Clark, Sharon A.
;
Ross, P. Joel
;
Meulenbroek, Robert A.
;
Maelandsmo, Gunhild M.
;
Parks, Robin J.
Genre
Journal Article
Abstract
Helper-dependent adenovirus (HD-Ad) vectors with all adenoviral genes deleted mediate very long-term expression of therapeutic transgenes in a...
Volume
78
Issue
11
Start Page
5966
DOI
10.1128/JVI.78.11.5966-5972.2004
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